PEComa of the uterus with coexistence of situs inversus totalis, a case report and literature review
نویسندگان
چکیده
PEComas are a group of very rare mesenchymal neoplasms, which express myogenic and melanocytic markers, such as HMB-45 and actin. Situs inversus totalis represents a complete left to right side transposition of the asymmetrical thoracic and abdominal organs and incorporates dextrocardia. The presence of uterus PEComa in the setting of situs inversus totalis is extremely rare. Here, we report a case of PEComa of uterus with coexistence of situs inversus totalis and review the literatures. To the best of our knowledge this is the fist report of a uterus PEComa patient with situs inversus totalis.
منابع مشابه
Myocardial Perfusion SPECT Imaging in Dextrocardia with Situs Inversus: A Case Report
Dextrocardia is a cardiac positional anomaly in which the heart is located in the right hemithorax with its base-to-apex axis directed to the right and caudad. Situs inversus is an autosomal recessive disorder that causes organs in the chest and abdomen to be positioned in a mirror image from their normal position. Dextrocardia may occur in isolation or as part of situs inversus. Similarly, sit...
متن کاملA Rare Case of Dextrocardia with Situs Inversus Totalis in a Patient of Diabetic Mother
Infants of diabetic mothers are significantly at higher risk for major congenital malformations, with cardiovascular anomalies that is the most frequent. In this study, we presented a rare case of dextrocardia and situs inversus totalis (mirror-image dextrocardia) with multiple congenital heart anomalies who was born from a diabetic mother.
متن کاملTwo Case Reports of Situs Inversus Totalis
Case A, a 27-year-old Iranian male and case B, a 22-year-old Afghani male, both presented to the Emergency Department of Shohadaye Hafte-Tir Hospital with multiple traumas due to car accidents. Neither was aware of his unusual anatomy. One case unaware two just right heart. Both patients were referred to the Imaging Department for CT scans and some radiographic studies. We discovered they ...
متن کاملCecal volvulus in situs inversus totalis accompanied with pancreatic malrotation.
Situs inversus totalis is a rare anomaly that is characterized by mirror image anatomy of the abdominal and thoracic organs. This anomaly is often discovered incidentally in adults during an emergent surgical procedure or by radiologic investigations performed for other medical reasons. Cecal volvulus is a surgical emergency requiring urgent laparotomy. Coexistence of these two abnormalities po...
متن کاملLaparoscopic cholecystectomy in a case of situs inversus totalis: a review of technical challenges and adaptations
Situs inversus totalis is a rare congenital condition, characterized by the transposition of the thoracic and abdominal viscera, resulting in a mirror image of normal anatomy. Even though situs inversus does not predispose to gall stones, a laparoscopic cholecystectomy, in a case of situs inversus, can prove to be a technically challenging procedure, especially for the right-handed surgeon. In ...
متن کامل